Good's Syndrome-Associated Pure Red Cell Aplasia with Myelodysplastic Syndrome
نویسندگان
چکیده
منابع مشابه
Myelodysplastic Syndrome with Erythroid Aplasia following Pure Red Cell Aplasia
Myelodysplastic syndrome (MDS) with erythroid aplasia is a very rare disorder that has not been clearly defined. We experienced a case of pure red cell aplasia (PRCA), which evolved to MDS with erythroid aplasia. A 59-year-old male with transfusion-dependent PRCA was referred to our hospital for an evaluation of newly developed thrombocytopenia. Two years ago, PRCA was diagnosed by the laborato...
متن کاملPure Red Cell Aplasia Associated with Good Syndrome
Pure red cell aplasia (PRCA) and hypogammaglobulinemia are paraneoplastic syndromes that are rarer than myasthenia gravis in patients with thymoma. Good syndrome coexisting with PRCA is an extremely rare pathology. We report the case of a 50-year-old man with thymoma and PRCA associated with Good syndrome who achieved complete PRCA remission after thymectomy and postoperative immunosuppressive ...
متن کاملRed cell aplasia in myelodysplastic syndrome.
Six cases of red cell aplasia occurring in patients with myelodysplastic syndromes (MDS) showed a diversity of clinical course and prognosis. In some patients red cell aplasia may have represented an evolution of MDS while in others autoimmune destruction of erythoblasts may have been the mechanism. A proliferative phase is seen in many of these patients, the clinical importance of which is unc...
متن کاملA patient with pure red cell aplasia and Good's syndrome.
ma, and hypogammaglobulinemia,2,5-8 however, no patient, except ours, was given a diagnosis of Good’s syndrome. In our case, anemia improved in response to immunosuppressive agents as it did in most of the other cases,2,5-8 but an increased frequency of various infections was seen, since Good’s syndrome is an immunodeficiency condition. Thymectomy normalized erythropoiesis in 1 out of 2 cases.7...
متن کاملPure red cell aplasia and associated thymoma
Pure red cell aplasia is a rare cause of anemia, caused by an absence of red blood cell precursors in the bone marrow. It is usually a paraneoplastic syndrome, associated most commonly with large-cell granular lymphocyte leukemia but also thymoma. For patients who present both pure red cell aplasia and thymoma, thymectomy leads to an initial remission of the aplasia in 30% of cases. However, su...
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ژورنال
عنوان ژورنال: Internal Medicine
سال: 2011
ISSN: 0918-2918,1349-7235
DOI: 10.2169/internalmedicine.50.5709